Evolution of Cellular Inclusions in Bietti’s Crystalline Dystrophy
Autor: | Chi-Chao Chan, J. Douglas Cameron, Emiko Furusato |
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Jazyk: | angličtina |
Rok vydání: | 2010 |
Předmět: |
Pathology
medicine.medical_specialty retina animal structures Posterior pole Review Biology crystalline retinopathy lcsh:Ophthalmology Cornea cornea medicine Bietti's crystalline dystrophy Bietti’s tapetoretinal dystrophy Retina Retinal pigment epithelium Dystrophy medicine.disease eye diseases medicine.anatomical_structure lcsh:RE1-994 embryonic structures Ultrastructure Bietti’s crystalline dystrophy Choroid sense organs |
Zdroj: | Ophthalmology and Eye Diseases, Vol 2010, Iss 2, Pp 9-15 (2010) Ophthalmology and Eye Diseases |
ISSN: | 1179-1721 |
Popis: | Bietti’s crystalline dystrophy (BCD) consists of small, yellow-white, glistening intraretinal crystals in the posterior pole, tapetoretinal degeneration with atrophy of the retinal pigment epithelium (RPE) and “sclerosis” of the choroid; in addition, sparking yellow crystals in the superficial marginal cornea are also found in many patients. BCD is inherited as an autosomal-recessive trait (4q35-tel) and usually has its onset in the third decade of life. This review focuses on the ultrastructure of cellular crystals and lipid inclusions of BCD. |
Databáze: | OpenAIRE |
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