Laryngeal involvement with fatal outcome in progressive nodular histiocytosis: A rare case report
| Autor: | Aarti S. Salunke, Vasudha A. Belgaumkar, Rinkesh Dobariya, Ravindranath B. Chavan |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2016 |
| Předmět: |
Pathology
medicine.medical_specialty Fatal outcome business.industry Case Report lcsh:RL1-803 medicine.disease Laryngeal involvement 03 medical and health sciences Non-Langerhans cell histiocytosis Histiocytosis 0302 clinical medicine 030228 respiratory system hemic and lymphatic diseases Rare case non-Langerhans cell histiocytosis medicine lcsh:Dermatology Histopathology 030212 general & internal medicine business nodules Progressive nodular histiocytosis |
| Zdroj: | Indian Dermatology Online Journal Indian Dermatology Online Journal, Vol 7, Iss 6, Pp 516-519 (2016) |
| ISSN: | 2249-5673 2229-5178 |
| Popis: | Progressive nodular histiocytosis (PNH) represents a very rare type of non-Langerhans cell histiocytosis. It is characterized by progressive appearance of papules and nodules without spontaneous resolution. We report a 60-year-old patient with novel clinical features in the form of extensive noduloulcerative lesions, ichthyotic patches, and laryngeal involvement culminating in fatal outcome prior to therapeutic intervention. Although the presenting features were baffling, histopathology and immunohistochemistry clinched the diagnosis of PNH. |
| Databáze: | OpenAIRE |
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