CT and MRI of Gorham Syndrome
| Autor: | G. Sigmund, B. Stöver, Hauenstein Kh, C. P. Adler, M O Tanyü, P. Vinee |
|---|---|
| Rok vydání: | 1994 |
| Předmět: |
Adult
Male medicine.medical_specialty Osteolysis Ischium medicine Humans Radiology Nuclear Medicine and imaging Femur Humerus Pelvic Bones Pelvis Pubic Bone medicine.diagnostic_test business.industry Infant Acetabulum Femur Head Magnetic resonance imaging Anatomy Middle Aged medicine.disease Magnetic Resonance Imaging Radiographic Image Enhancement medicine.anatomical_structure Shoulder Fractures Vascular channel Female Osteolysis Essential Radiology Presentation (obstetrics) Tomography X-Ray Computed business Follow-Up Studies |
| Zdroj: | Journal of Computer Assisted Tomography. 18:985-989 |
| ISSN: | 0363-8715 |
| DOI: | 10.1097/00004728-199411000-00028 |
| Popis: | Gorham syndrome, also known as massive osteolysis or vanishing bone, is a rare disorder (135 cases reported) leading to extensive loss of bony matrix, replaced by proliferating thin-walled vascular channels. Three histologically proven cases of the disease are reported, including the clinical presentation and modern imaging features with CT (with 3D reconstruction) as well as T1- and T2-weighted MRI. Two cases in young women were located in the pelvis with extensive osteolysis reaching to the acetabulum. The third case in a 2-month-old boy is the youngest case ever reported and involved the humerus. The radiological appearance of the disease is discussed and the importance of the modern imaging methods debated. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|