A life-threatening presentation of eosinophilic granulomatosis with polyangiitis

Autor: Maria Frigerio, Patrizia Pedrotti, Francesco Musca, Arash Astaneh, Jan Walter Schroeder, Fabrizio Oliva, Claudio Russo, Manlio Cipriani, Edgardo Bonacina, Sandra Nonini, Enrico Ammirati, Alberto Roghi
Rok vydání: 2016
Předmět:
Adult
Male
Pathology
medicine.medical_specialty
Time Factors
Biopsy
medicine.medical_treatment
Shock
Cardiogenic

Churg-Strauss Syndrome
030204 cardiovascular system & hematology
Necrosis
03 medical and health sciences
Extracorporeal Membrane Oxygenation
0302 clinical medicine
Refractory
Eosinophilic
medicine
Extracorporeal membrane oxygenation
Humans
heterocyclic compounds
cardiovascular diseases
030212 general & internal medicine
medicine.diagnostic_test
business.industry
Myocardium
Cardiogenic shock
Granulomatosis with Polyangiitis
General Medicine
medicine.disease
Magnetic Resonance Imaging
Myocarditis
Treatment Outcome
Shock (circulatory)
Administration
Intravenous

Steroids
Presentation (obstetrics)
medicine.symptom
Cardiology and Cardiovascular Medicine
business
Granulomatosis with polyangiitis
Immunosuppressive Agents
Zdroj: Journal of Cardiovascular Medicine. 17:e109-e111
ISSN: 1558-2027
Popis: Necrotizing eosinophilic myocarditis (NEM) is a life-threatening condition that needs rapid diagnosis by endomyocardial biopsy and hemodynamic support usually by mechanical circulatory systems. We present the case of a 25-year-old Caucasian man who developed a refractory cardiogenic shock due to a NEM that was supported with a peripheral veno-arterial extracorporeal membrane oxygenation associated with intravenous steroids and recovered after 2 weeks. Further instrumental investigations lead to the final diagnosis of NEM as first presentation of eosinophilic granulomatosis with polyangiitis (formerly Churg-Strauss syndrome), remarking the importance of identifying the systemic disorder that usually triggers the eosinophilic damage of the myocardium.
Databáze: OpenAIRE