Oral manifestations and rehabilitation of a patient with osteogenesis imperfecta
| Autor: | Milena Milanovic, Olivera Jovicic, Milos Beloica, Bojan Janjic, Zoran Mandinic, Jelena Juloski |
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| Rok vydání: | 2021 |
| Předmět: |
Pediatrics
medicine.medical_specialty Rehabilitation business.industry medicine.medical_treatment rare diseases osteogenesis imperfecta General Medicine medicine.disease partial dentures 3. Good health stomatognathic diseases 03 medical and health sciences 0302 clinical medicine stomatognathic system Osteogenesis imperfecta medicine Medicine 030212 general & internal medicine business dentinogenesis imperfecta |
| Zdroj: | Srpski Arhiv za Celokupno Lekarstvo, Vol 149, Iss 11-12, Pp 708-712 (2021) |
| ISSN: | 2406-0895 0370-8179 |
| DOI: | 10.2298/sarh210722083m |
| Popis: | Introduction. Osteogenesis imperfecta is a rare heritable connective tissue disorder characterized by increased fragility of the bony tissue. The incidence of orofacial alterations associated with osteogenesis imperfecta is variable and includes dentinogenesis imperfecta, malocclusions, hypoplasia of the jaws, delayed dental development and structural abnormalities of the teeth. Case outline. A 22-year-old female was referred to the Clinic for Pediatric and Preventive Dentistry for dental treatment. Enlarged head, triangular-shaped face, mandibular prognathism with excessive maxillary hypoplasia, lowered vertical occlusal dimension were present features. The intraoral findings included dentinogenesis imperfecta with Kennedy?s class IV in the upper jaw and class II in the lower jaw. Panoramic radiograph revealed abnormalities in the crown and root shape, obliteration of the pulp chamber and severe deficiency of alveolar bone mass. Overall treatment involved five phases: I ? preventive and prophylactic treatment, II ? direct restauration of five teeth with glass ionomer cement, III ? extraction of severely damaged teeth, IV ? prosthodontic rehabilitation with removable partial dentures, V ? maintenance and follow-up phase. Conclusion. Low prevalence and wide variety of signs and symptoms make dental treatment of osteogenesis imperfecta overly complex and challenging. Nevertheless, it is essential to improve craniofacial and dental function along with facial aesthetic. |
| Databáze: | OpenAIRE |
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