Cerebral venous drainage via the ophthalmic veins in the Sturge-Weber syndrome
| Autor: | Z. Bak, B. Baráth, E. Vörös, M. Bodosi |
|---|---|
| Rok vydání: | 1994 |
| Předmět: |
Adult
Intracranial Arteriovenous Malformations medicine.medical_treatment Sturge–Weber syndrome Veins Neoplasms Multiple Primary Fatal Outcome Ptosis Sturge-Weber Syndrome medicine Humans Radiology Nuclear Medicine and imaging Cerebellar Neoplasms Vein Melanoma Craniotomy medicine.diagnostic_test business.industry Anatomy Angiomatosis medicine.disease Magnetic Resonance Imaging Hypoplasia Cerebral Angiography medicine.anatomical_structure Angiography cardiovascular system Female Neurology (clinical) medicine.symptom Tomography X-Ray Computed Cardiology and Cardiovascular Medicine business Cerebral angiography |
| Zdroj: | Neuroradiology. 36:318-320 |
| ISSN: | 1432-1920 0028-3940 |
| DOI: | 10.1007/bf00593271 |
| Popis: | We describe a 23-year-old girl with an extremely uncommon form of cerebral venous drainage and cerebellar leptomeningeal angiomatosis as a possible variant of the Sturge-Weber syndrome. Extensive congenital port-wine stains all over the body, hypoplastic left renal and subclavian and iliac veins, cardiomegaly and ptosis and hypoplasia of the left kidney had been recognised in early childhood. She rapidly developed signs of intracranial hypertension. CT and MRI showed a right medial temporal lesion. Angiography revealed cerebellar pial angiomatosis with enlarged medullary veins and no functioning sigmoid sinuses or jugular veins. Cerebral venous drainage was via enlarged ophthalmic veins. Although the intracranial venous abnormalities were characteristic of the Sturge-Weber syndrome anomalies beyond the encephalofacial territory suggested a more complex developmental abnormality. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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