Surgical treatment of retrosternal extraosseous Ewing Sarcoma in a 6-years old female: a clamshell approach with hemysternectomy and application of a non-crosslinked extracellular matrix
| Autor: | Luca Luzzi, Amalia Schiavetti, Giulia Varrasso, Francesco Molinaro, Piero Paladini, Anna Clerico, Chiara Pellegrino, Mario Messina, Leonardo Casini, Rossella Angotti |
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| Jazyk: | angličtina |
| Rok vydání: | 2017 |
| Předmět: |
Clamshell
medicine.medical_specialty lcsh:Surgery 030204 cardiovascular system & hematology Pediatrics Extracellular matrix 03 medical and health sciences 0302 clinical medicine Neuroblastoma medicine Surgical treatment Lung Extraosseous Ewing Sarcoma business.industry Pediatrics Perinatology and Child Health Surgery lcsh:RJ1-570 Soft tissue lcsh:Pediatrics lcsh:RD1-811 Perinatology and Child Health medicine.disease lung incision children medicine.anatomical_structure 030220 oncology & carcinogenesis Sarcoma business |
| Zdroj: | Journal of Pediatric Surgery Case Reports, Vol 22, Iss C, Pp 9-13 (2017) |
| Popis: | Background Ewing Sarcoma (ES) and Neuroblastoma (NB) belong to a family of tumours of primitive neuroectodermal origin (PNET) that occurs in both bone and soft tissue. Notwithstanding ES and NB are two distinct malignant tumours, sometimes there could be a link between them. Case report We describe a case of an extraosseous ES localized in the retrosternal region and the upper lobe of the right lung, which had been previously treated for NB in a 6 years old female. We treated this case with a clamshell approach which allows, in a one-step surgery, a complete excision of the mass reconstructing the hemysternectomy with a non-crosslinked matrix. Conclusion the clamshell approach is therefore useful to achieve the retrosternal space and the lung with a single surgical access. According to our experience, we consider appropriate to use a non-crosslinked matrix for sternal reconstruction. |
| Databáze: | OpenAIRE |
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