Duodenal atresia with apple-peel configuration of the ileum and absent superior mesenteric artery
Autor: | Radović V. Saša, Crnogorac Snezana, Suhih Djordje, Lazovic Ranko, Banjac Lidija |
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Jazyk: | angličtina |
Předmět: |
Male
medicine.medical_specialty Vascular Malformations Vacular accident Intestinal Atresia Apple peel Case Report Ileum Infant Premature Diseases Apple-peel atresia 030230 surgery Gastroenterology Duodenal atresia 03 medical and health sciences Fatal Outcome 0302 clinical medicine Mesenteric Artery Superior Internal medicine medicine.artery medicine Humans Abnormalities Multiple Superior mesenteric artery Pediatrics Perinatology and Child Health business.industry digestive oral and skin physiology Infant Newborn medicine.disease medicine.anatomical_structure Apple peel atresia Atresia Pediatrics Perinatology and Child Health Gestation Duodenal Obstruction business Infant Premature 030217 neurology & neurosurgery |
Zdroj: | BMC Pediatrics |
ISSN: | 1471-2431 |
DOI: | 10.1186/s12887-016-0690-y |
Popis: | Background Embryologically, duodenal atresia results from inadequate recanalisation and proliferation of gut epithelius in the 6th week of gestation, while apple-pee atresia of small bowel is a consequence of a vascular accident in subsequent embryonic development, and the two are rather rarely manifested as a joint clinical entity. Case presentation We present here a 29 week preterm boy admitted to the intensive care unit due to breathing difficulties and low birthweight. Following clinical, radiographic and ultrasound examination, he was diagnosed with duodenal obstruction and subjected to surgical treatment. The exploration of abdominal cavity verified duodenal atresia in the second portion with the absence of third and fourth portions of duodenum, superior mesenteric artery, as well as apple-peel atresia of jejunum. Resection of the apple-peel segment of jejunum was done and the continuity of digestive tube was established by the end-to-end duodeno-ileal anastomosis. Conslusion This rare case of ours questions the embryology of duodenal atresia suggesting that a mesenteric vascular disruption phenomenon in subsequent embryonic life might be the aetiological factor. |
Databáze: | OpenAIRE |
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