Single-Ventricle Palliation in a 4-Year-Old With Ehlers-Danlos Syndrome
| Autor: | Eric R. Griffiths, Aaron W. Eckhauser, Zach M. DeBoard |
|---|---|
| Rok vydání: | 2018 |
| Předmět: |
Male
Pulmonary and Respiratory Medicine medicine.medical_specialty Connective tissue Unbalanced atrioventricular canal defect 030204 cardiovascular system & hematology 03 medical and health sciences 0302 clinical medicine medicine Humans Atrioventricular valve business.industry Palliative Care Neoaortic root medicine.disease Surgery medicine.anatomical_structure 030228 respiratory system Ventricle Ehlers–Danlos syndrome Child Preschool Ehlers-Danlos Syndrome Cardiology and Cardiovascular Medicine business Preoperative imaging |
| Zdroj: | The Annals of Thoracic Surgery. 105:e31-e32 |
| ISSN: | 0003-4975 |
| DOI: | 10.1016/j.athoracsur.2017.08.027 |
| Popis: | We report the case of a 4-year-old boy with Ehlers-Danlos syndrome undergoing single-ventricle palliation for an unbalanced atrioventricular canal defect. No reports of single-ventricle palliation in the setting of connective tissue disorders exist in the current literature. Unique findings on the patient's preoperative imaging included a disproportionately large neoaortic root and a regurgitant atrioventricular valve, which may foretell the need for future intervention. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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