Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome
| Autor: | Carlos A. Cañas, Fabio Bonilla-Abadía, Manuel A. Pérez, Joaquín D. Rosales, Evelyn Muñoz-Buitrón, Gabriel J. Tobón |
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| Rok vydání: | 2013 |
| Předmět: |
Exocrine gland
Pathology medicine.medical_specialty Parotid gland enlargement lcsh:Diseases of the musculoskeletal system business.industry Healthy population Case Report MALT lymphoma General Medicine medicine.disease Blastoid Variant Mantle Cell Lymphoma eye diseases Lymphoma stomatognathic diseases medicine.anatomical_structure stomatognathic system immune system diseases hemic and lymphatic diseases ORAL DRYNESS Medicine lcsh:RC925-935 Sjogren s business |
| Zdroj: | Case Reports in Rheumatology, Vol 2013 (2013) Case Reports in Rheumatology |
| ISSN: | 2090-6897 2090-6889 |
| Popis: | Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-fold compared to healthy population, mainly of the MALT lymphoma type. This case reports a 52-year-old woman with pSS developing a progressively growing mass at face and neck compatible with blastoid variant mantle cell lymphoma and a fatal outcome. |
| Databáze: | OpenAIRE |
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