Relapsing polychondritis with isolated tracheal involvement and airway‐only symptoms
| Autor: | Lili Cheng, Chia Tse Weng, Tang Hsiu Huang, Sheng Yuan Wang |
|---|---|
| Rok vydání: | 2020 |
| Předmět: |
Pulmonary and Respiratory Medicine
Pathology medicine.medical_specialty Case Report Case Reports 03 medical and health sciences 0302 clinical medicine Bronchoscopy medicine tracheal stenosis Relapsing polychondritis lcsh:RC705-779 medicine.diagnostic_test Dry cough business.industry Pneumocystis jirovecii Pneumonia lcsh:Diseases of the respiratory system respiratory system Exertional dyspnoea medicine.disease Tracheal Stenosis 030228 respiratory system central airway obstruction 030220 oncology & carcinogenesis Chest radiograph Airway business |
| Zdroj: | Respirology Case Reports, Vol 8, Iss 7, Pp n/a-n/a (2020) Respirology Case Reports |
| ISSN: | 2051-3380 |
| Popis: | Relapsing polychondritis (RP) is a rare autoimmune disorder, characterized by the inflammation of cartilaginous structures and proteoglycan‐rich tissues. Due to its rarity and the notoriously variable presentations, the diagnosis of RP could be challenging. We report an unusual case of RP with isolated tracheal involvement and very non‐specific symptoms of exertional dyspnoea and dry cough. The initial chest radiograph showed long‐segment narrowing of the trachea, and the computed tomography of the chest revealed thickened cartilaginous walls of the trachea, while the posterior membranous portion was spared. The tracheal narrowing was readily observed under bronchoscopy. The patient was treated with oral prednisolone. Although the subsequent course was transiently complicated by an episode of severe Pneumocystis jirovecii pneumonia with acute respiratory distress syndrome, the patient overall responded well to systemic corticosteroid therapy. No new symptoms developed during a two‐year follow‐up. We describe an atypical case of relapsing polychondritis that involved solely the tracheal cartilages and presented clinically as non‐specific airway symptoms. Timely diagnosis and treatment through a multidisciplinary approach is crucial to prevent subsequent serious complications. |
| Databáze: | OpenAIRE |
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