Chest wall volumes, diaphragmatic mobility, and functional capacity in patients with mucopolysaccharidoses

Autor: Bárbara Bernardo Figueirêdo, Cyda Reinaux, Helen Fuzari, António Sarmento, Juliana Fernandes, Armèle Dornelas de Andrade
Rok vydání: 2022
Předmět:
Zdroj: Disability and rehabilitation.
ISSN: 1464-5165
Popis: We investigated respiratory muscle strength, diaphragm mobility, lung function, functional capacity, quality of life, body composition, breathing pattern, and chest wall (A cross-sectional study with data analyzed separately according to age group. A total of 68 individuals (34 MPS and 34 matched-healthy subjects) were included. Six-minute walking test assessed functional capacity and ultrasound assessed diaphragm mobility during quiet spontaneous breathing (QB). Optoelectronic plethysmography assessedBody composition, lung function, respiratory muscle strength, and functional capacity were reduced in MPS (allLung function, respiratory muscle strength, functional capacity, diaphragm mobility, and quality of life are reduced in MPS compared with matched healthy subjects.
Databáze: OpenAIRE