Systemic juvenile xanthogranulomatosis imitating a malignant abdominal wall tumor with lung metastases
| Autor: | Pramila Ramani, Keith Sibson, Savvas Andronikou, David Grier, Nicola J. Matcham |
|---|---|
| Rok vydání: | 2007 |
| Předmět: |
Pathology
medicine.medical_specialty Systemic disease Lung Neoplasms Tomography Scanners X-Ray Computed Juvenile xanthogranuloma Malignancy Benign tumor Abdominal wall medicine Humans Abdominal Neoplasms False Positive Reactions Neoplasm Metastasis Lung Neoplasms/*radiography/secondary Sarcoma/radiography Lung business.industry Abdominal Wall Sarcoma Hematology medicine.disease Radiography medicine.anatomical_structure Abdominal Neoplasms/*radiography Oncology Xanthogranuloma Juvenile/*radiography Child Preschool Pediatrics Perinatology and Child Health Female business Xanthogranuloma Juvenile |
| Zdroj: | Journal of pediatric hematology/oncology. 29(1) |
| ISSN: | 1077-4114 |
| Popis: | Juvenile xanthogranulomatosis (JXG) is a rare benign condition, which usually presents with characteristic skin lesions and can be diagnosed clinically. However, systemic JXG may involve a wide range of extracutaneous sites and may pose a diagnostic dilemma for the clinician, radiologist, and pathologist. In particular it may simulate malignancy. Here, we report a case of systemic JXG within the abdominal wall musculature and lungs, which imitated a sarcoma with pulmonary metastases on computerized tomography. To the best of our knowledge, this is the first such reported case. In particular, systemic disease presenting without skin lesions is unusual. J Pediatr Hematol Oncol |
| Databáze: | OpenAIRE |
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