Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report

Autor: Krešimir Bulić, Sanja Konosić, Ruža Grizelj, Tomislav Luetić, Ivica Sjekavica, Sanja Pleško, Anko Antabak, Dalibor Šarić, Nada Sindičić Dessardo, Ana Marija Alduk, Jurica Vuković, Tomislav Ćaleta, Karolina Režek Tomašić, Danko Mikulić
Rok vydání: 2019
Předmět:
Zdroj: Croatian Medical Journal
Volume 60
Issue 4
ISSN: 1332-8166
0353-9504
Popis: Conjoined twining is a rare medical phenomenon, with an overall prevalence of 1.47 per 100000 births. This report describes a successful separation of xypho-omphalopa- gus conjoined twins complicated by unbalanced blood shunting through the porto- systemic anastomoses within the shared liver parenchyma. Significant extrauterine twin- twin transfusion syndrome caused by unbalanced shunt- ing is an extremely rare, and probably under- recognized, hemodynamic complication in conjoined twins necessi- tating urgent separation. Progressive deterioration with a poor outcome can be prevented if the condition is recog- nized in a timely manner.
Databáze: OpenAIRE