Recurrent metastatic primary inflammatory myofibroblast tumour of the gallbladder following pancreaticoduodenectomy
| Autor: | Malary Mani, Roi Anteby, Benjamin Golas, Brianne Sullivan |
|---|---|
| Rok vydání: | 2020 |
| Předmět: |
medicine.medical_specialty
medicine.medical_treatment Pancreaticoduodenectomy Metastasis Diagnosis Differential 03 medical and health sciences 0302 clinical medicine Rare Disease Surgical oncology Humans Medicine Neoplasm Metastasis Myofibroblasts Mesentery Aged 80 and over business.industry Gallbladder Soft tissue General Medicine medicine.disease medicine.anatomical_structure 030220 oncology & carcinogenesis Female Gallbladder Neoplasms 030211 gastroenterology & hepatology Radiology Neoplasm Recurrence Local Gallbladder Neoplasm business Myofibroblast |
| Zdroj: | BMJ Case Rep |
| ISSN: | 1757-790X |
| DOI: | 10.1136/bcr-2019-232861 |
| Popis: | Inflammatory myofibroblast tumour (IMT) is an uncommon soft tissue tumour with an unpredictable clinical course: mostly benign, occasionally locally aggressive and rarely capable of metastasis. Diagnosed mainly in the mesentery, omentum, retroperitoneum, pelvis and lungs, IMT is extremely rare as a primary gallbladder tumour. Despite improved radiographical capabilities, differentiating the tumour from other more common causes of gallbladder neoplasms necessitates histopathological and immunohistochemistry tests. Once diagnosed, malignant potential should be taken into consideration, striving for an en bloc R0 resection and postoperative long-term follow-up with routine ancillary imaging. The authors present the case of a recurrent primary IMT of the gallbladder, after two surgical treatments, including a pancreaticoduodenectomy. Now 3 years after initial diagnoses the patient is asymptomatic, but has developed local and distant metastases and is being treated with systemic corticosteroid. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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