Rapid spontaneous regression of multicentric infantile myofibromatosis in the posterior fossa and lumbar vertebra
| Autor: | Masaharu Akiyama, Yuki Yuza, Tomoru Miwa, Hikaru Sasaki, Yuichi Yokokawa, Shizuo Oi, Kentaro Yokoi, Hiroyuki Ida, Ryo Tamogami, Yuichiro Nonaka |
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| Rok vydání: | 2010 |
| Předmět: |
Male
medicine.medical_specialty Infantile myofibromatosis Lumbar vertebrae Skull Base Neoplasms Myofibromatosis Lesion Lumbar Biopsy medicine Humans Lumbar Vertebrae Spinal Neoplasms medicine.diagnostic_test business.industry Infant Newborn General Medicine medicine.disease Magnetic Resonance Imaging Surgery Radiography medicine.anatomical_structure Cranial Fossa Posterior Neoplasm Regression Spontaneous Pediatrics Perinatology and Child Health Neurology (clinical) Neurosurgery medicine.symptom business Subcutaneous tissue |
| Zdroj: | Child's Nervous System. 27:491-496 |
| ISSN: | 1433-0350 0256-7040 |
| Popis: | Infantile myofibromatosis is the most common fibrous tumor of infancy and early childhood. It typically occurs in skin, subcutaneous tissue, muscle, bone, and/or viscera. In patients without visceral involvement, the prognosis is excellent, generally with spontaneous regression of the tumor nodules in 1 to 2 years [1]. However, they show unfavorable prognosis within the first few months of life if there is visceral involvement [1]. Intracranial involvement is rare, and to our knowledge, only 17 such cases have been reported [1–15]. Although lesions usually arise from the dura [16] and grow in one direction, either epidural or subdural, in our case, there was equal growth epidurally and subdurally. Spontaneous regression occurred at the same time as that of a lumbar lesion 3 months after biopsy. This unique course has never been reported, and the rate of regression in this case was remarkable. Case report |
| Databáze: | OpenAIRE |
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