Unusual histological variant of malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation

Autor:	Sachin B Ingle, Pushkar P. Matkari, Saroj Bolde, Gopal Pandit, Smita Shete
Rok vydání:	2015
Předmět:	Poor prognosis Pathology medicine.medical_specialty business.industry Malignant triton tumor Soft tissue Case Report Malignant peripheral nerve sheath tumor General Medicine medicine.disease medicine Immunohistochemistry In patient Desmin Neurofibromatosis business
Zdroj:	World Journal of Clinical Cases. 3:389
ISSN:	2307-8960
DOI:	10.12998/wjcc.v3.i4.389
Popis:	Malignant peripheral nerve sheath tumor (MPNST) with rhabdomyoblastic differentiation is called as malignant triton tumor (MTT). It is highly aggressive soft tissue tumor with higher local recurrence rate. MTT has poor prognosis than MPNST. MTT seems to be more aggressive in patients with neurofibromatosis (NF-1). We herein, reporting an interesting case of 55 years male with multiple neurofibromas all over the body since 30 years and multiple café-au-lait spots, diagnosed as NF-1. Since 6 years, he had an enlarged mass in left thigh. Wide excision of mass was done. On histopathological examination revealed the diagnosis of MTT and diagnosis of which was confirmed on immunohistochemistry.
Databáze:	OpenAIRE
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