Pulmonary Fibrosis in Children

Autor: Guillaume Thouvenin, Chiara Sileo, Hubert Ducou Le Pointe, Effrosyne Manali, Nadia Nathan, Aurore Coulomb L'Hermine, Annick Clement, Laura Berdah, Pierre-Louis Leger, Spyros Papiris, Céline Delestrain
Přispěvatelé: Service de Pneumologie pédiatrique [CHU Trousseau], CHU Trousseau [APHP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Physiopathologie des maladies génétiques d'expression pédiatrique (UMRS_933), Sorbonne Université (SU)-Institut National de la Santé et de la Recherche Médicale (INSERM), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), National and Kapodistrian University of Athens (NKUA), Service de pathologie [CHU Trousseau], Maladies génétiques d'expression pédiatrique (U933), Institut National de la Santé et de la Recherche Médicale (INSERM)-CHU Trousseau [APHP], COST Action European network for translational research in children's and adult interstitial lung disease (COST-ILD) project CA16125Legs Poix from the Chancellerie des Universites, Paris 1305, 1405, 1015, 2077, DP2017/1860European Commission 305653Respirer c'est GrandirBelleherbe Association, ANR-10-COHO-0003,RADICO,Cohorte nationale maladies rares(2010), European Project: 305653,EC:FP7:HEALTH,FP7-HEALTH-2012-INNOVATION-1,CHILD-EU(2012)
Jazyk: angličtina
Rok vydání: 2019
Předmět:
Zdroj: Journal of Clinical Medicine
Journal of Clinical Medicine, MDPI, 2019, 8 (9), pp.1312. ⟨10.3390/jcm8091312⟩
Journal of Clinical Medicine, Vol 8, Iss 9, p 1312 (2019)
Journal of Clinical Medicine, 2019, 8 (9), pp.1312. ⟨10.3390/jcm8091312⟩
ISSN: 2077-0383
DOI: 10.3390/jcm8091312⟩
Popis: International audience; Pulmonary fibrosis (PF) is a very rare condition in children, which may be observed in specific forms of interstitial lung disease. None of the clinical, radiological, or histological descriptions used for PF diagnosis in adult patients, especially in situations of idiopathic PF, can apply to pediatric situations. This observation supports the view that PF expression may differ with age and, most likely, may cover distinct entities. The present review aims at summarizing the current understanding of PF pathophysiology in children and identifying suitable diagnostic criteria. View Full-Text
Databáze: OpenAIRE