Wunderlich’s Syndrome, or Spontaneous Retroperitoneal Hemorrhage, in a Patient with Tuberous Sclerosis and Bilateral Renal Angiomyolipoma
| Autor: | Carlos Casimiro, Júlio Constantino, Liliana Duarte, Sara Catarino Santos, Jorge Pereira, Fernando Valerio |
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| Rok vydání: | 2017 |
| Předmět: |
Adult
medicine.medical_specialty Angiomyolipoma Exploratory laparotomy medicine.medical_treatment Hemorrhage Nephrectomy 030218 nuclear medicine & medical imaging Benign tumor 03 medical and health sciences Tuberous sclerosis 0302 clinical medicine Tuberous Sclerosis medicine Humans Retroperitoneal space Retroperitoneal Space Hemoperitoneum Retroperitoneal hemorrhage business.industry food and beverages Syndrome Articles General Medicine medicine.disease Kidney Neoplasms medicine.anatomical_structure Female Radiology medicine.symptom business 030217 neurology & neurosurgery |
| Zdroj: | The American Journal of Case Reports |
| ISSN: | 1941-5923 |
| Popis: | Patient: Female, 33 Final Diagnosis: Renal angiomyolipoma Symptoms: Abdominal discomfort Medication: — Clinical Procedure: — Specialty: Surgery Objective: Rare disease Background: Wunderlich’s syndrome, or spontaneous non-traumatic retroperitoneal hemorrhage, can be a life-threatening event. Renal angiomyolipoma is a rare benign tumor that can occur sporadically, or in association with tuberous sclerosis. A case of spontaneous retroperitoneal hemorrhage in a patient with tuberous sclerosis and bilateral renal angiomyolipoma is presented. Case Report: A 33-year-old female Caucasian patient, with a known medical history of tuberous sclerosis, was admitted to hospital as an emergency, with right-sided abdominal pain. Abdominal computed tomography (CT) imaging showed bilateral renal tumors, consistent with bilateral renal angiomyolipoma. The larger tumor, involving the enlarged right kidney (24.0 cm in length), had a diameter of 21.0 cm and was associated with hemoperitoneum and retroperitoneal hemorrhage, and contrast ‘blush’ on CT confirmed arterial bleeding. An initial urgent exploratory laparotomy with renal packing was initially performed, but right nephrectomy was required for hemorrhage control. The patient was discharged from hospital on the 23rd postoperative day, without further complications. Conclusions: This report describes a case of Wunderlich’s Syndrome, or spontaneous retroperitoneal hemorrhage, in a patient with tuberous sclerosis and bilateral renal angiomyolipoma, presenting as an emergency. An early diagnosis and timely treatment are important in cases of retroperitoneal hemorrhage to prevent life-threatening complications. |
| Databáze: | OpenAIRE |
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