Plexiform neurofibromatosis involving face and oral cavity
| Autor: | Hema Gopalaiah, Gajendra Veeraraghavan, Selvaraj Sunantha, Dorairaj Jayachandran |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2014 |
| Předmět: |
Neurofibromatosis type I
medicine.medical_specialty Café- au- lait macules peripheral nerve sheath tumor business.industry Soft tissue Malignant peripheral nerve sheath tumor Case Report medicine.disease Oral cavity Disfigurement Dermatology Pathology and Forensic Medicine Surgery Otorhinolaryngology facial plexiform neurofibromatosis Plexiform neurofibroma Medicine Neurofibromatosis von Recklinghausen's business Complication General Dentistry |
| Zdroj: | Journal of Oral and Maxillofacial Pathology : JOMFP |
| ISSN: | 1998-393X 0973-029X |
| Popis: | Plexiform neurofibromas (PNFs) are one of the most common and debilitating complications of neurofibromatosis type I (NF-I). They account for substantial morbidity, disfigurement, functional impairment and are life threatening. PNFs can also be subjected to transformation into malignant peripheral nerve sheath tumor (MPNST). This complication is refractory to treat due to paucity of effective therapies for malignant soft tissue sarcomas in general and also the delay in diagnosis from a preexisting tumor. We report a case of PNF of face involving oral cavity with literature review. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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