The sunflower cataract in Wilson’s disease: pathognomonic sign or rare finding?
| Autor: | Karolina Dzieżyc, Ewa Langwińska-Wośko, Anna Członkowska, Tomasz Litwin |
|---|---|
| Rok vydání: | 2015 |
| Předmět: |
Adult
Male medicine.medical_specialty Visual acuity Adolescent Wilson’s disease Clinical Neurology Diagnostic Techniques Ophthalmological Cataract Diagnosis Differential Lens Young Adult 03 medical and health sciences 0302 clinical medicine Hepatolenticular Degeneration Humans Medicine In patient Kayser–Fleischer ring business.industry Diagnostic algorithms General Medicine Middle Aged medicine.disease Dermatology Sunflower cataract Surgery Wilson's disease 030221 ophthalmology & optometry Original Article Female Neurology (clinical) Pathognomonic sign Differential diagnosis medicine.symptom business Copper 030217 neurology & neurosurgery |
| Zdroj: | Acta Neurologica Belgica |
| ISSN: | 2240-2993 0300-9009 |
| DOI: | 10.1007/s13760-015-0566-1 |
| Popis: | The presence of Kayser-Fleischer ring in patients with Wilson's disease (WD) is well documented and included in diagnostic algorithms; however, data about the occurrence of the second postulated ophthalmological sign of WD, sunflower cataract (SC), are limited and even conflicting. The aim of our study was to verify the occurrence of SC in WD. From January 2010 to May 2015, 81 consecutive, newly diagnosed WD patients underwent detailed ophthalmological examinations, including slit lamp examination with special attention to lens transparency, to verify the presence of SC in WD-naive patients. SC was detected in only one (1.2 %) of the examined WD patients, did not impact visual acuity; moreover, completely disappeared following a year of treatment for WD. SC may be a very rare and reversible ophthalmological manifestation of WD that is observed seldom and only at the time of WD diagnosis. We postulate that a finding of SC in WD patients is an interesting finding that may occur in the course of WD, but it is not a pathognomonic sign of WD. |
| Databáze: | OpenAIRE |
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