Noncoronary sinus of Valsalva rupture into the right atrium with a coexisting perimembranous ventricular septal defect
Autor: | David Hannon, Long-Bao Cao, Assad Movahed |
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Jazyk: | angličtina |
Rok vydání: | 2013 |
Předmět: |
medicine.medical_specialty
congenital hereditary and neonatal diseases and abnormalities business.industry Perimembranous ventricular septal defect Case Report General Medicine medicine.disease Surgery Stenosis medicine.anatomical_structure Bicuspid valve Ehlers–Danlos syndrome Ventricle Internal medicine medicine Cardiology cardiovascular system Right atrium cardiovascular diseases business Coronary sinus Sinus (anatomy) |
Popis: | Ruptured sinus of Valsalva is very uncommon, and is < 1% of all congenital defects. The incidence ranges from 0.1%-3.5%. There is a male to female predominance of 4:1, with the highest incidence in the Asian population. Higher incidence is also seen in patients with Marfan's syndrome and Ehlers Danlos syndrome. There is a higher association of ruptured sinus of Valsalva with ventricular septal defect (VSD), aortic stenosis, and bicuspid valve defect. While most patients with VSD often have rupture of their right coronary sinus of Valsalva into the right ventricle due to poor structural integrity, we present a rare case of a patient with VSD who had rupture of his noncoronary sinus of Valsalva into the right atrium. |
Databáze: | OpenAIRE |
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