Mounier-Kuhn syndrome: A variable course disease
| Autor: | Saoussen Cheikh Mhammed, Ahmed Ben Saad, Lobna Loued, S. Joobeur, Asma Achour, Asma Migaou, Nesrine Fahem, Naceur Rouatbi |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2020 |
| Předmět: |
Pulmonary and Respiratory Medicine
Tracheobronchomegaly Pediatrics medicine.medical_specialty Case Report Disease Tracheal diverticulum 03 medical and health sciences 0302 clinical medicine Bronchoscopy medicine Respiratory function Respiratory system Computed tomography lcsh:RC705-779 medicine.diagnostic_test business.industry lcsh:Diseases of the respiratory system medicine.disease Mounier-Kuhn syndrome 030228 respiratory system Respiratory failure 030220 oncology & carcinogenesis business Rare disease |
| Zdroj: | Respiratory Medicine Case Reports Respiratory Medicine Case Reports, Vol 31, Iss, Pp 101238-(2020) |
| ISSN: | 2213-0071 |
| Popis: | Mounier-Kuhn syndrome or tracheobronchomegaly is a rare disease characterized by marked dilation of the trachea and proximal bronchi with recurrent lower tract respiratory infections. Computed tomography and bronchoscopy are the key tools to accomplish the diagnosis. This is a condition with a clinical polymorphism, symptoms vary from minor with preserved respiratory function, to very severe with life threatening exacerbations leading to respiratory failure and premature death. The treatment is mainly symptomatic, stenting or surgery are reserved to extreme cases.Herein, we report two cases of the same condition with different clinical signs and diverse outcome. |
| Databáze: | OpenAIRE |
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