Post-operative airway obstruction in Noonan syndrome: An unusual presentation
| Autor: | Hemalata R Iyer, Sheetal R Jagtap, Rochana G Bakhshi, Hemant N Lahoti |
|---|---|
| Rok vydání: | 2015 |
| Předmět: |
Pediatrics
medicine.medical_specialty business.industry respiratory system Airway obstruction Brief Communication medicine.disease Short stature Surgery lcsh:RD78.3-87.3 Anesthesiology and Pain Medicine lcsh:Anesthesiology Atlantoaxial instability medicine Webbed neck Noonan syndrome Presentation (obstetrics) medicine.symptom Craniofacial Airway business |
| Zdroj: | Indian Journal of Anaesthesia Indian Journal of Anaesthesia, Vol 59, Iss 7, Pp 442-444 (2015) |
| ISSN: | 0019-5049 |
| DOI: | 10.4103/0019-5049.160961 |
| Popis: | Noonan syndrome (NS) is an autosomal dominant disorder with craniofacial, cardiac, skeletal abnormalities, haemorrhagic diathesis, with reported incidence of 1 in 1000 to 1 in 2500 live births.[1] Various lymphatic abnormalities have been observed in these patients including pulmonary and intestinal lymphangiectasia and lymphoedema.[2] Craniofacial dysmorphism webbed neck and atlantoaxial instability can complicate airway management.[3] The anaesthetic considerations include difficult airway, impaired cardio-pulmonary function, mental retardation, and short stature. We report an unusual presentation of airway obstruction due to bronchial cast on 5th post-operative day in a case of NS, who underwent laparoscopic orchidopexy. |
| Databáze: | OpenAIRE |
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