Long-term survival without surgical intervention in a patient with a natural history of a single right ventricle: A case report

Autor: Kana Kubota, Koichi Kataoka, Masaaki Kawada, Kazuomi Kario, Gaku Ohki, Yusuke Ishiyama, Yasushi Imai
Rok vydání: 2021
Předmět:
Zdroj: J Cardiol Cases
ISSN: 1878-5409
DOI: 10.1016/j.jccase.2020.12.013
Popis: Single ventricle (SV), a complex cardiac anomaly, if left untreated, is thought to lead to a poor prognosis. Herein, we report the case of a long-term survivor with an unrepaired SV with right ventricle (RV) morphology. A 55-year-old man presented with a SV with RV morphology, with a double outlet, large atrial septal defect, common atrioventricular valve, pulmonary valve stenosis (PS), and dextrocardia. Because the native PS provided adequate restriction of the pulmonary blood flow, he did not develop pulmonary hypertension; however, he had severe cyanosis. In patients with SV and moderate PS, even if the SV has RV morphology, long-term survival may be possible without surgical intervention.
Databáze: OpenAIRE