Osteogenesis Imperfecta Congenita and Tarda: A Temporal Bone Report
| Autor: | Joan T. Zajtchuk, John R. Lindsay |
|---|---|
| Rok vydání: | 1975 |
| Předmět: |
Male
Deafness Stapes Surgery 03 medical and health sciences Dogs Fetus 0302 clinical medicine Temporal bone medicine Animals Humans 030223 otorhinolaryngology Endochondral ossification Fenestration Labyrinth Cochlea Aged Ear Ossicles business.industry Infant Newborn Temporal Bone Prostheses and Implants General Medicine Anatomy Osteogenesis Imperfecta OSTEOGENESIS IMPERFECTA CONGENITA medicine.disease Stapes Conductive hearing loss Footplate Stapes Mobilization Otosclerosis Otorhinolaryngology Osteogenesis imperfecta tarda 030220 oncology & carcinogenesis Female Vestibule Labyrinth business |
| Zdroj: | Annals of Otology, Rhinology & Laryngology. 84:350-358 |
| ISSN: | 1943-572X 0003-4894 |
| DOI: | 10.1177/000348947508400311 |
| Popis: | The temporal bone report of an operated case of osteogenesis imperfecta tarda is presented. Histological examination confirmed the presence of bilateral fixation of the footplate by otosclerosis as the cause of the conductive hearing loss. Fragility of bony septae in the mastoid and of the stapedial crura were observed. Sensorineural impairment in later years with a reduction in neural elements in the cochlea appear related to the extent and activity of the otosclerotic foci. Additional temporal bone reports of three cases of osteogenesis imperfecta congenita show lack of deposition of the skein-like bone in the endochondral layer, sparse bony septae in marrow spaces and deficiency of the periosteal layer. The stapedial crura were thin and in two cases both were deformed and fractured. |
| Databáze: | OpenAIRE |
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