MALOCCLUSION AND DENTAL GROWTH DISORDERS: DIAGNOSTIC CRITERIA OR CLINICAL MANIFESTATIONS OF HEREDITARY CONNECTIVE TISSUE DISORDERS?
| Autor: | E. V. Timofeev, S. G. Galstyan, E. V. Zemtsovsky |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2021 |
| Předmět: |
Marfan syndrome
medicine.medical_specialty dental growth disorders Benign joint hypermobility Science Loeys–Dietz syndrome stickler syndrome AZ20-999 medicine ehlers-danlos syndrome loeys-dietz syndrome Stickler syndrome business.industry Diagnostic algorithms malocclusion Marfanoid habitus medicine.disease Dermatology hereditary disorders of connective tissue facial dysmorphia Ehlers–Danlos syndrome Medicine History of scholarship and learning. The humanities Malocclusion business marfan syndrome connective tissue dysplasia |
| Zdroj: | Juvenis Scientia, Vol 7, Iss 4, Pp 22-31 (2021) |
| ISSN: | 2414-3790 2414-3782 |
| Popis: | Currently, hereditary connective tissue disorders (HCTD) are divided into hereditary syndromes - rare diseases that are diagnosed according to internationally agreed criteria (Marfan, Ehlers-Danlos, Stickler, Loeys-Dietz syndromes, and others), and a number of dysplastic phenotypes (marfanoid habitus, marfan-like and Ehlers-like phenotypes, benign joint hypermobility). The involvement of the bone system in the dysplastic process is typical for most HCTD. The bone signs of dysembriogenesis include malocclusion and dental growth disorders. The article presents an overview of current recommendations for a number of HCTD, assesses the role of facial signs of dysembriogenesis in the diagnostic algorithms for these diseases. A rather low prognostic value of such signs as malocclusion and dental growth disorders in the detection of hereditary syndromes and dysplastic phenotypes is shown. The clinical manifestations of HCTD in the maxillofacial region are analyzed - the frequent detection of different types of the malocclusion and dental growth disorders in HCTD is demonstrated. The difficulties of orthodontic treatment of patients with hereditary syndromes are substantiated. |
| Databáze: | OpenAIRE |
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