Mucosal linear IgA disease with esophageal involvement responsive to ustekinumab
| Autor: | Kristin M. Leiferman, Danny Varedi, Christina Topham, Amber Jimenez, Christopher M. Hull |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2021 |
| Předmět: |
medicine.medical_specialty
Linear IgA bullous dermatosis Mucocutaneous zone Case Report Dermatology Disease ustekinumab Rare case Ustekinumab Medicine Direct fluorescent antibody integumentary system Linear IgA disease treatment business.industry BMZ basement membrane zone LABD linear IgA bullous dermatosis medicine.disease immunobullous dermatosis RL1-803 DIF direct immunofluorescence linear IgA bullous dermatosis business medicine.drug Blistering disease |
| Zdroj: | JAAD Case Reports JAAD Case Reports, Vol 15, Iss, Pp 4-6 (2021) |
| ISSN: | 2352-5126 |
| Popis: | Linear IgA bullous dermatosis (LABD), or linear IgA disease, is a rare autoimmune mucocutaneous blistering disease with vesicles and bullae characteristically arranged in an annular or arciform pattern on the skin and, less common, mucosal involvement manifesting as vesicles, erosions, and/or ulcers. We present a rare case of a patient who had Crohn's disease and LABD with primarily mucosal involvement, including oral, esophageal, and vaginal lesions, who responded well to ustekinumab therapy. |
| Databáze: | OpenAIRE |
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