Type I aortopulmonary window presenting with very early onset Eisenmenger's syndrome

Autor: Jayaranganath Mahimarangaiah, Navin Agrawal, Soumya Patra, Cholenhally Nanjappa Manjunath
Rok vydání: 2014
Předmět:
Zdroj: BMJ case reports. 2014
ISSN: 1757-790X
Popis: A 2-year-old child with a history of recurrent chest infection early in infancy presented with clubbing, cyanosis, oxygen saturation of 86% in room air, left parasternal heave, short ejection systolic murmur at left second space and loud pulmonary component of second heart sound suggestive of severe pulmonary hypertension. X-ray revealed cardiomegaly with pulmonary artery dilation and peripheral vasoconstriction (figure 1). Echocardiography revealed biventricular hypertrophy with moderate tricuspid regurgitation and pulmonary artery systolic pressure of 90 mm Hg. A large aortopulmonary (AP) window (1 cm) was demonstrated in the parasternal short axis view with bidirectional shunting (figures 2⇓–4, videos 1⇓–3). Cardiac catheterisation to assess for the reversibility of the …
Databáze: OpenAIRE