Acquired Angioedema: A Rare Manifestation of Angioimmunoblastic T Cell Lymphoma
| Autor: | Nita Rachel Rajan, Santosh K Dasar, Ravikala Rao, Ashok S. Naik, Vijay G. Bidkar |
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| Rok vydání: | 2017 |
| Předmět: |
Pathology
medicine.medical_specialty Angioimmunoblastic T-cell lymphoma High index medicine.medical_treatment Acquired angioedema Lymph node biopsy 03 medical and health sciences 0302 clinical medicine Medicine skin and connective tissue diseases 030223 otorhinolaryngology Clinical Report Angioedema medicine.diagnostic_test business.industry Immunosuppression medicine.disease Dermatology Otorhinolaryngology Tongue swelling 030220 oncology & carcinogenesis Surgery medicine.symptom Age of onset business |
| Zdroj: | Indian J Otolaryngol Head Neck Surg |
| ISSN: | 0973-7707 2231-3796 |
| DOI: | 10.1007/s12070-017-1122-5 |
| Popis: | The clinical presentation except age of onset is similar in different types of angioedema. A lymphoproliferative disorder like angioimmunoblastic T cell lymphoma (AITL) rarely presents with symptoms of angioedema. We present extremely rare case of elderly male with recurrent tongue swelling, pruritus with normal levels of complements and C1 esterase inhibitor protein featuring as acquired angioedema, a rare manifestation of AITL. Initial response to corticosteroids may be misleading and occurs as a result of immunosuppression of AITL. High index of suspicion may prompt need for histopathological diagnosis of lymph node biopsy. Definitive chemotherapeutic treatment may achieve long term remission. |
| Databáze: | OpenAIRE |
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