Rectal atresia and stenosis: unique anorectal malformations

Autor: Miller Hamrick, Emily Louden, Marc A. Levitt, Alberto Peña, Andrea Bischoff, Bala Eradi
Rok vydání: 2012
Předmět:
Zdroj: Journal of Pediatric Surgery. 47:1280-1284
ISSN: 0022-3468
Popis: Introduction Rectal atresia/stenosis is a rare disorder in the spectrum of anorectal malformations and is particularly associated with a presacral mass. These patients are born with a normal anal canal but have a stricture or complete atresia located a few centimeters proximal to the dentate line. We present a surgical technique for the management of these patients, as well as their unique clinical concerns and outcomes. Methods We reviewed the records of 14 patients with rectal atresia and 3 with rectal stenosis. We describe a novel technique that we have developed for the preservation of the anterior dentate line that was performed in the last 13 patients. Results Rectal atresia/stenosis was associated with a presacral mass in 5 patients (29%). Definitive repair was completed using a circular rectorectal anastomosis in the first 4 patients and an anterior dentate line sparing procedure in the last 13. All patients older than 3 years have demonstrated the ability to have voluntary bowel movements. Conclusion With the largest reported series of rectal atresia/stenosis, we have demonstrated a safe and effective technique for repair. Preoperative evaluation must be thorough because a significant number of these patients will have an associated presacral mass.
Databáze: OpenAIRE