Japanese clinical practice guidelines for allied disorders of Hirschsprung's disease, 2017
| Autor: | Satoshi Obata, Takeshi Tomomasa, Yoshio Watanabe, Shinsuke Onuma, Satoshi Ieiri, Atsuyuki Yamataka, Yuko Araki, Tomoya Fukuoka, Wataru Sumita, Kosuke Ushijima, Hiroshi Tamai, Masahiro Yoshida, Akio Kubota, Akira Toki, Suguru Fukahori, Masanori Tamura, Naoki Shimojima, Tomoaki Taguchi, Takahiro Jimbo, Yoshimitsu Fujii, Toshio Morizane, Toshihiko Watanabe, Kouji Masumoto, Genshiro Esumi, Hiroshi Matsufuji, Ken Haruma, Keisuke Jimbo, Haruhiko Sago, Hideki Sou, Hiroyuki Kobayashi, Fujimi Kawai, Tatsuo Kuroda, Tomoko Yamasaki, Masaki Nio, Yoshinori Hamada, Atsushi Nakajima, Yoshiyuki Yamada, Shin Fukudo, Shunsuke Nosaka, Takahiro Kudo, Yutaka Kanamori, Mitsuru Muto |
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| Rok vydání: | 2017 |
| Předmět: |
medicine.medical_specialty
Future studies Colon Intestinal biopsy Urinary Bladder Medical information Disease Distribution system Diagnosis Differential 03 medical and health sciences 0302 clinical medicine Japan Daily practice medicine Humans Abnormalities Multiple Hirschsprung Disease Intensive care medicine Hirschsprung's disease business.industry Intestinal Pseudo-Obstruction medicine.disease Clinical Practice 030220 oncology & carcinogenesis Pediatrics Perinatology and Child Health 030211 gastroenterology & hepatology business |
| Zdroj: | Pediatrics international : official journal of the Japan Pediatric Society. 60(5) |
| ISSN: | 1442-200X |
| Popis: | Background Despite the presence of ganglion cells in the rectum, some patients have symptoms similar to those of Hirschsprung's disease. A consensus has yet to be established regarding the terminology for these diseases. We defined this group of diseases as "allied disorders of Hirschsprung's disease" and compiled these guidelines to facilitate accurate clinician diagnosis and provide appropriate treatment strategies for each disease. Methods These guidelines were developed using the methodologies in the Medical Information Network Distribution System (MINDS). Of seven allied disorders, isolated hypoganglionosis; megacystis-microcolon-intestinal hypoperistalsis syndrome; and chronic idiopathic intestinal pseudo-obstruction were selected as targets of clinical questions (CQ). In a comprehensive search of the Japanese- and English-language articles in PubMed and Ichu-Shi Web, 836 pieces of evidence related to the CQ were extracted from 288 articles; these pieces of evidence were summarized in an evidence table. Results We herein outline the newly established Japanese clinical practice guidelines for allied disorders of Hirschsprung's disease. Given that the target diseases are rare and intractable, most evidence was drawn from case reports and case series. In the CQ, the diagnosis, medication, nutritional support, surgical therapy, and prognosis for each disease are given. We emphasize the importance of full-thickness intestinal biopsy specimens for the histopathological evaluation of enteric ganglia. Considering the practicality of the guidelines, the recommendations for each CQ were created with protracted discussions among specialists. Conclusions Clinical practice recommendations for allied disorders of Hirschprung's disease are given for each CQ, along with an assessment of the current evidence. We hope that the information will be helpful in daily practice and future studies. |
| Databáze: | OpenAIRE |
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