Polysplenia with agenesis of the dorsal pancreas and preduodenal portal vein, about a case
| Autor: | Abdelaziz Fadil, Khalid Elhattabi, Fatimazahra Bensardi, Othmane Elyamine, Abdelilah el bakouri, Mounir Bouali |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2020 |
| Předmět: |
medicine.medical_specialty
PV portal vein Polysplenia syndrome Portal vein Case Report PS polysplenia syndrome 03 medical and health sciences Gastric adenocarcinoma 0302 clinical medicine IVC inferior vena cava medicine Agenisis of the dorsal pancreas Lack of knowledge Polysplenia business.industry medicine.disease BA biliary atresia Total gastrectomy 030220 oncology & carcinogenesis Agenesis 030211 gastroenterology & hepatology Surgery Radiology business Preduodenal portal vein Dorsal pancreas |
| Zdroj: | International Journal of Surgery Case Reports |
| ISSN: | 2210-2612 |
| Popis: | Highlights • Polysplenia is a complex polymalformative syndrome that includes a spectrum of visceral and vascular anatomical abnormalities; extremely undiscovered in adulthood. • A rare case of polysplenia syndrome showing an exceptional association between preduodenal portal vein, dorsal pancreas agenesis and polysplenia on gastric adenocarcinoma. • Surgeons must be aware of their possible existence and be able to recognize them to avoid major intraoperative injuries. • Surgeons must have a perfect knowledge of the reference anatomy and the exploration of anatomical variations in imaging before surgical exploration. • PDPV is believed to pose increased risk to gastric cancer patients during gastrectomy and lymph node dissection around the hepatoduodenal ligament. Purpose of the study Polysplenia is a complex polymalformative syndrome that is frequently accompanied by an inconsistent spectrum of visceral and vascular anatomical abnormalities and is extremely undiscovered in adulthood. The objective of this article is to limit the intraoperative risks generated by the lack of knowledge of these anatomical variations by insisting on the inconstancy of all these variations and the perfect knowledge of the reference anatomy and the exploration of the anatomical variations in imaging before the surgery. Patient and methods The patient was 50-year-old who was hospitalized in our department for gastric adenocarcinoma. During her extension assessment, a polysplenia syndrome was accidentally discovered on the scan images, which showed an exceptional association between preduodenal portal vein, agenesis of the dorsal pancreas, and polysplenia. Conclusion There are neither specific clinical symptoms of the polysplenia syndrome, nor any biological sign; hence, the interest of recognizing this pathology is to avoid diagnostic errors, but also to guide the surgeon during the surgical act performed. |
| Databáze: | OpenAIRE |
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