Unilateral Congenital Facial Nerve Paralysis Secondary to a Benign Epithelioid Peripheral Nerve Sheath Tumor

Autor: Javad Towfighi, Jon E. Isaacson, Todd W. Preston, Michael P. Ondik
Rok vydání: 2007
Předmět:
Zdroj: Otology & Neurotology. 28:1091-1093
ISSN: 1531-7129
DOI: 10.1097/mao.0b013e318158828f
Popis: Objective A benign epithelioid peripheral nerve sheath tumor is described in the setting of congenital facial nerve (FN) paralysis. This is the first reported case in the English literature. Patient A 10-month-old girl with unilateral congenital FN paralysis. Interventions Auditory brainstem evoked potential study, gadolinium-enhanced magnetic resonance imaging, temporal bone computed tomography, and transmastoid FN decompression with tumor resection. Main outcome measures Follow-up for tumor recurrence and postoperative FN function. Results The child underwent a transmastoid FN exploration with resection of a 0.6-cm spherical tumor analyzed to be a benign epithelioid peripheral nerve sheath tumor. There is no evidence of recurrence, and FN function was unchanged at 1 year postoperatively. Conclusion Benign epithelioid peripheral nerve sheath tumor can cause congenital facial nerve palsy.
Databáze: OpenAIRE