Intermediate Follow-up and Management of Previously Reported Malignant Peripheral Nerve Sheath Tumor of the Penis
| Autor: | Daniel R. McMahon, Eric Z. Massanyi, Hannah Agard, Ananth S. Murthy, Curtis J. Clark, Neel Parekh |
|---|---|
| Rok vydání: | 2020 |
| Předmět: |
Male
medicine.medical_specialty Urologic Surgical Procedures Male Urology medicine.medical_treatment 030232 urology & nephrology Aftercare Malignant peripheral nerve sheath tumor Nerve Sheath Neoplasms 03 medical and health sciences 0302 clinical medicine Urethra medicine Humans Neurofibromatosis Child Penile Neoplasms Chemotherapy Adjuvant radiotherapy Penectomy business.industry Genitourinary system Soft tissue Plastic Surgery Procedures medicine.disease Neoadjuvant Therapy Treatment Outcome medicine.anatomical_structure 030220 oncology & carcinogenesis Scrotum Radiology business Penis |
| Zdroj: | Urology. 135:133-135 |
| ISSN: | 0090-4295 |
| DOI: | 10.1016/j.urology.2019.09.028 |
| Popis: | Malignant peripheral nerve sheath tumors (MPNSTs) are soft tissue sarcomas that arise from peripheral nerve fibers and primarily occur in the setting of neurofibromatosis (NF1). MPNST arising from the penis is very rare and may require mutilating surgery to achieve surgical cure. We previously reported a case of MPNST involving the penis in a 14-month-old boy treated with neoadjuvant chemotherapy, total penectomy, and adjuvant radiation. Here we report intermediate follow-up of the same patient, describe his subsequent genitourinary reconstruction, and discuss management dilemmas that arise following treatment of penile MPNST. |
| Databáze: | OpenAIRE |
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