Plexiform neurofibroma of the oesophagus: a mimicker of malignancy
| Autor: | H De'Costa, Z Soonawalla, Arul Ganeshan, L Q Hon |
|---|---|
| Rok vydání: | 2005 |
| Předmět: |
Male
Pathology medicine.medical_specialty Neurofibromatosis 1 Esophageal Neoplasms Malignancy Resection Diagnosis Differential Pathognomonic Plexiform neurofibroma medicine Humans Neurofibroma Radiology Nuclear Medicine and imaging Esophagus Neurofibromatosis Aged Neurofibroma Plexiform business.industry General Medicine medicine.disease Dysphagia medicine.anatomical_structure sense organs medicine.symptom Tomography X-Ray Computed business |
| Zdroj: | The British Journal of Radiology. 78:1095-1097 |
| ISSN: | 1748-880X 0007-1285 |
| DOI: | 10.1259/bjr/28935759 |
| Popis: | We report the first case of a plexiform neurofibroma of the oesophagus, presenting with dysphagia in a 67-year-old man known to suffer from von Recklinghausen's neurofibromatosis. The clinical symptoms and radiological findings mimicked malignancy, and raised considerable concern. Numerous investigations failed to elucidate the benign nature of the condition. The diagnosis was finally achieved at surgery and the patient was successfully treated by oesophageal resection. Plexiform neurofibromas, though only found in 20-30% of affected individuals are pathognomonic of von Recklinghausen's neurofibromatosis. This report highlights the tendency of plexiform neurofibromas to grow extensively and encase surrounding structures, thereby mimicking a neoplastic process. |
| Databáze: | OpenAIRE |
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