Thoracic Duct Decompression for Protein-Losing Enteropathy in Failing Fontan Circulation

Autor: Isabel Fragata, Marta Antonio, Andreia Gordo, Fátima Pinto, Conceicao Pereira, José Fragata
Rok vydání: 2015
Předmět:
Male
Decompression
medicine.medical_treatment
Vasodilator Agents
Decompression
Surgical/methods
Heart Defects
Congenital/surgery
030204 cardiovascular system & hematology
Fontan Procedure
HSM CAR PED
Protein-Losing Enteropathies/surgery
0302 clinical medicine
Adrenal Cortex Hormones
Hypoplastic Left Heart Syndrome
Enteropathy
Protein-Losing Enteropathies/etiology
Atrium (heart)
Atrioventricular Block
HSM ANS
Lymphatic System/physiopathology
Brachiocephalic Veins
Protein losing enteropathy
Heart Atria/diagnostic imaging
Cardiac Pacing
Artificial
Decompression
Surgical
Combined Modality Therapy
medicine.anatomical_structure
Lymphatic system
Pulmonary Veins
cardiovascular system
Cardiology
Vasodilator Agents/therapeutic use
Female
Cardiology and Cardiovascular Medicine
Pulmonary and Respiratory Medicine
Heart Defects
Congenital
medicine.medical_specialty
Heart Atria/surgery
Vena Cava
Superior
Adolescent
Protein-Losing Enteropathies
Pulmonary Veins/surgery
Adrenal Cortex Hormones/therapeutic use
HSM CCT
Norwood Procedures
Thoracic duct
Fontan circulation
Thoracic Duct
Lymphatic System
03 medical and health sciences
Atrioventricular Block/etiology
Internal medicine
medicine
Atrioventricular Block/therapy
Humans
cardiovascular diseases
Heart Atria
Brachiocephalic Veins/diagnostic imaging
business.industry
Fontan Procedure/adverse effects
Brachiocephalic Veins/surgery
medicine.disease
Surgery
Vena Cava
Superior/surgery
030228 respiratory system
Norwood procedure
Thoracic Duct/surgery
business
Tomography
X-Ray Computed
Hypoplastic Left Heart Syndrome/surgery
Zdroj: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Agência para a Sociedade do Conhecimento (UMIC)-FCT-Sociedade da Informação
instacron:RCAAP
ISSN: 1552-6259
Popis: An infrequent but devastating late complication of Fontan circulation is protein-losing enteropathy (PLE), which results from unbalanced lymphatic homeostasis. Surgical decompression of the thoracic duct by redirecting its drainage to the pulmonary venous atrium has been introduced recently as a possible treatment. This report describes a single-institution experience with this innovative procedure in 2 patients with failing Fontan circulation with PLE refractory to optimized medical therapy.
Databáze: OpenAIRE
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