Desmoid-type fibromatosis of the head and neck in children: a case report and review of the literature
| Autor: | Tomoya Soma, Hidetaka Miyashita, Taneaki Nakagawa, Masaki Yazawa, Hiromasa Kawana, Kanako Munakata, Seiji Asoda |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2016 |
| Předmět: |
medicine.medical_specialty
Case Report Desmoid type fibromatosis Fibromatosis Surgical Flaps 03 medical and health sciences Head and neck 0302 clinical medicine Tongue Surgical oncology medicine Humans Tongue Neoplasm Desmoid Children Medicine(all) business.industry Infant General Medicine Debulking medicine.disease Surgery Tongue Neoplasms body regions Fibromatosis Aggressive medicine.anatomical_structure Treatment Outcome 030220 oncology & carcinogenesis Female business 030217 neurology & neurosurgery Decision-making |
| Zdroj: | Journal of Medical Case Reports |
| ISSN: | 1752-1947 |
| Popis: | Background Desmoid-type fibromatosis is defined as an intermediate tumor that rarely occurs in the head and neck of children. There is no doubt as to the value of complete surgical excision for desmoid-type fibromatosis. However, in pediatric patients, surgeons may often be concerned about making a wide excision because of the potential for functional morbidity. Some studies have reported a lack of correlation between margin status and recurrence. Therefore, we discussed our findings with a focus on the state of surgical margins. Case presentation We report an unusual case of a 9-month-old Japanese girl who prior to presenting at our hospital underwent debulking surgery twice with chemotherapy for desmoid-type fibromatosis of the tongue at another hospital. We performed a partial glossectomy and simultaneous reconstruction with local flap and achieved microscopic complete resection. We also reviewed available literature of pediatric desmoid-type fibromatosis in the head and neck. Conclusions We described successful treatment for the refractory case of pediatric desmoid-type fibromatosis. The review results showed that some microscopic incomplete resections of tumors in pediatric patients with desmoid-type fibromatosis tended to be acceptable with surgical treatment. |
| Databáze: | OpenAIRE |
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