Omovertebral bone associated with Sprengel deformity and Klippel-Feil syndrome leading to cervical myelopathy
| Autor: | Philipp Tanner, Lars Füllbier, Nikolai J. Hopf, Hans Henkes |
|---|---|
| Rok vydání: | 2010 |
| Předmět: |
Adult
medicine.medical_specialty Decompression Klippel–Feil syndrome Spinal Cord Diseases Myelopathy Deformity Humans Medicine Spinal canal Bone growth business.industry General Medicine medicine.disease Magnetic Resonance Imaging Osteotomy Surgery Scapula Urinary Incontinence medicine.anatomical_structure Klippel-Feil Syndrome Cervical Vertebrae Etiology Ataxia Female medicine.symptom Tomography X-Ray Computed business Rare disease |
| Zdroj: | Journal of Neurosurgery: Spine. 13:224-228 |
| ISSN: | 1547-5654 |
| DOI: | 10.3171/2010.3.spine09665 |
| Popis: | The unusual association of an omovertebral bone with Sprengel deformity and Klippel-Feil syndrome is a complex bone anomaly of unknown incidence and etiology. However, several cases of this rare disease pattern have been reported in the literature. In this paper, the authors present the case of a 34-year-old woman with a 5-month history of progressive gait ataxia and intermittent urinary incontinence, which was found to be caused by aberrant bone growth into the spinal canal from an omovertebral bone that extended from the left scapula pressing into the C-6 vertebral arch and subsequently causing cervical myelopathy. The patient underwent isolated resection of the omovertebral bone and decompression of the spinal canal, and her functional and neurological outcome was favorable. |
| Databáze: | OpenAIRE |
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