Cochlear implants in the management of hearing loss in Neurofibromatosis Type 2
| Autor: | Yu Chuen Tam, Neil Donnelly, Patrick R. Axon, Nicola Folland, James R. Tysome, Frances Harris, Zebunnisa H Vanat, Gemma Crundwell, Juliette Durie-Gair, Richard D. Knight |
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| Rok vydání: | 2017 |
| Předmět: |
Adult
Male Neurofibromatosis 2 medicine.medical_specialty Adolescent Referral Hearing loss medicine.medical_treatment Acoustic neuroma Audiology Schwannoma Auditory Brain Stem Implantation Young Adult 03 medical and health sciences Speech and Hearing 0302 clinical medicine Cochlear implant Evoked Potentials Auditory Brain Stem otorhinolaryngologic diseases medicine Humans Neurofibromatosis type 2 Hearing Loss 030223 otorhinolaryngology Aged Retrospective Studies Aged 80 and over Vestibular system business.industry Patient Selection Middle Aged medicine.disease Cochlear Implantation Cochlear Implants Treatment Outcome Otorhinolaryngology Speech Perception Female medicine.symptom business 030217 neurology & neurosurgery Auditory brainstem implant |
| Zdroj: | Cochlear Implants International. 18:171-179 |
| ISSN: | 1754-7628 1467-0100 2009-2016 |
| DOI: | 10.1080/14670100.2017.1300723 |
| Popis: | Review of cochlear implant (CI) outcomes in patients with Neurofibromatosis Type 2 (NF2), implanted in the presence of an ipsilateral vestibular schwannoma (VS). Hearing restoration was combined in some cases with a Bevacizumab regime.Retrospective review of 12 patients, managed over the period 2009-2016, at a tertiary referral multidisciplinary NF2 clinic. The patients are grouped by hearing outcomes to explore likely protective factors, and to generate a proposed decision-making tool for the selection of either CI or Auditory Brainstem Implant (ABI).Four of the 12 patients achieved speech discrimination without lip-reading. In these individuals there is reason to think that the mechanism of their hearing loss was cochlear dysfunction. A further four patients received benefit to lip-reading and awareness of environmental sound. For such patients their hearing loss may have been due to both cochlear and neural dysfunction. Two patients gained access to environmental sound only from their CI. Two patients derived no benefit from their CIs, which were subsequently explanted. Both these latter patients had had prior ipsilateral tumour surgery, one just before the CI insertion.Cochlear implantation can lead to open set speech discrimination in patients with NF2 in the presence of a stable VS. Use of promontory stimulation and intraoperative electrically evoked auditory brainstem response testing, along with case history, can inform the decision whether to implant an ABI or CI. |
| Databáze: | OpenAIRE |
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