Sporadic, Nontrauma-Related, Desmoid Tumor of the Pancreas: A Rare Disease—Case Report and Literature Review
| Autor: | E. D'Amore, G. Costantin, F. Polistina, Giovanni Ambrosino |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2010 |
| Předmět: |
Pathology
medicine.medical_specialty medicine.diagnostic_test business.industry lcsh:R Cancer lcsh:Medicine Case Report General Medicine medicine.disease Asymptomatic Familial adenomatous polyposis medicine.anatomical_structure Gardner Syndrome Biopsy medicine Immunohistochemistry medicine.symptom Pancreas business Rare disease |
| Zdroj: | Case Reports in Medicine, Vol 2010 (2010) Case Reports in Medicine |
| ISSN: | 1687-9635 1687-9627 |
| Popis: | Desmoid tumors (DTs) are neoplasms of fibroblastic origin characterized by lack of a capsule. They are nonmetastatic and locally aggressive. Intraabdominal DTs are often observed in familial adenomatous polyposis and Gardner syndrome or subsequent to localized traumatic injury. Sporadic forms are defined as nontrauma- or nongenetic-related DTs. Isolated, sporadic pancreatic DTs have been considered anecdotal, with only 9 cases described in the literature. We report the case of a 68-year-old man with a case of sporadic cystic DT localized to the pancreatic tail. The tumor was discovered incidentally during computerized tomography performed for an unrelated condition. The patient was asymptomatic; however, biopsy was performed on the clinical suspicion of cystic cancer of the pancreas. Pathology analysis showed fibroblastic proliferation, and the diagnosis of DT was confirmed by immunohistochemical staining for beta-catenin. The patient underwent resection with no further treatment and remain disease-free 60 months after surgery. |
| Databáze: | OpenAIRE |
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