Familial Mediterranean fever associated frosted branch angiitis, retinal vasculitis and vascular occlusion
| Autor: | Harry Petrushkin, Remzi Karadag, Ilknur Tugal-Tutkun, Hilal Eser-Ozturk, Maurizio Battaglia Parodi, Errol W. Chan, Soukaina Belfaiza, Pinar Cakar Ozdal, F. Nilüfer Yalçındağ, Hana A Mansour, Sirel Gür Güngör, Ahmad M. Mansour, Sibel Kadayifcilar |
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| Rok vydání: | 2021 |
| Předmět: |
Male
Adult medicine.medical_specialty Adolescent Familial Mediterranean fever Vascular occlusion Dexamethasone Young Adult Branch retinal artery occlusion medicine Humans Fluorescein Angiography Retrospective Studies Retinal Vasculitis Retinal Vascular Occlusion business.industry Retinal vasculitis General Arts and Humanities medicine.disease Dermatology Sensory Systems Familial Mediterranean Fever Ophthalmology Central retinal artery occlusion Female medicine.symptom Colchicine business Vasculitis Uveitis |
| Zdroj: | Eye. 36:2157-2162 |
| ISSN: | 1476-5454 0950-222X |
| DOI: | 10.1038/s41433-021-01822-5 |
| Popis: | OBJECTIVES To analyse the entity of retinal vasculitis, including frosted branch angiitis (FBA), or retina vascular occlusion in patients with familial Mediterranean fever (FMF). METHODS Retrospective collaborative case series using invitation by email to uveitis specialists around the Mediterranean basin. This series was combined with a literature review. Exclusion criteria included infectious diseases, Behcet's disease or other autoimmune diseases. RESULTS A total of 16 patients (21 eyes) had FMF and retinal vasculitis (FBA 11 patients, mild retinal vasculitis 5 patients). The mean age at onset of vasculitis was 29.5 ± 13.4 (range 9-62) with a female to male ratio of 9 to 7. In 19 eyes treated with various forms of corticosteroid and/or immunosuppression, the mean initial spectacle-corrected visual acuity improved from 6/194 to 6/10.5 at the last mean follow-up of 29.0 ± 34.9 months (p |
| Databáze: | OpenAIRE |
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