Technical Considerations for Lung Transplantation in Kartagener’s Syndrome
| Autor: | Bryan F. Meyers, Elbert P. Trulock, Ramsey R. Hachem, Benjamin D. Kozower, Chad A. Witt, G. Alexander Patterson, Roger D. Yusen, Steven L. Brody, Patrick R. Aguilar, Andrew J. Bierhals, Varun Puri, Derek E. Byers, Jason M. Gauthier, Ruben G. Nava, Daniel Kreisel, Tsuyoshi Takahashi |
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| Rok vydání: | 2019 |
| Předmět: |
Male
Pulmonary and Respiratory Medicine congenital hereditary and neonatal diseases and abnormalities medicine.medical_specialty medicine.medical_treatment 030204 cardiovascular system & hematology 03 medical and health sciences 0302 clinical medicine otorhinolaryngologic diseases medicine Humans Lung transplantation Dextrocardia Cardiopulmonary Bypass S syndrome Bronchiectasis Kartagener Syndrome business.industry Genetic disorder Pulmonary situs inversus Middle Aged respiratory system medicine.disease respiratory tract diseases Situs inversus 030228 respiratory system Surgery Radiology Cardiology and Cardiovascular Medicine business Airway Lung Transplantation |
| Zdroj: | The Annals of Thoracic Surgery. 107:e337-e339 |
| ISSN: | 0003-4975 |
| Popis: | Kartagener's syndrome is a rare genetic disorder of ciliated epithelial cells associated with recurrent respiratory tract infections, bronchiectasis, and situs inversus. In some patients, the accumulation of airway secretions and recurrent infections lead to end-stage lung disease, for which lung transplantation is the only effective treatment. Anatomical variations, such as dextrocardia and pulmonary situs inversus, make the procedure challenging, yet feasible with certain technical modifications and careful preparation of donor lungs. We report a case of bilateral lung transplantation without the use of cardiopulmonary bypass in a patient with Kartagener's syndrome while describing important technical details of the operation. |
| Databáze: | OpenAIRE |
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