Takayasu's arteritis associated with Wiskott-Aldrich syndrome
| Autor: | W M Lawton, Yu-Lung Lau, Sik Nin Wong |
|---|---|
| Rok vydání: | 1992 |
| Předmět: |
Male
Hypertensive encephalopathy medicine.medical_specialty business.industry Takayasu's arteritis Lymphocyte proliferation medicine.disease Renal artery stenosis Gastroenterology Takayasu Arteritis Renovascular hypertension Surgery Wiskott-Aldrich Syndrome Aortic aneurysm Internal medicine Child Preschool Pediatrics Perinatology and Child Health medicine Humans Arteritis business Immunodeficiency |
| Zdroj: | Journal of paediatrics and child health. 28(5) |
| ISSN: | 1034-4810 |
| Popis: | A unique case of a Chinese boy with Wiskott-Aldrich syndrome (WAS) associated with Takayasu's arteritis is reported. He had eczema, epistaxis and recurrent infections since early infancy and was found to have thrombocytopenia, negative delayed-type skin hypersensitivity, low T cell number and impaired lymphocyte proliferation to phytohaemagglutinin and concanavalin A. He had high normal serum immunoglobulin (Ig)G and IgA with low IgM and isohaemagglutinin. He presented with hypertensive encephalopathy at 5.5 years of age and an aortogram demonstrated abdominal aortic aneurysm with bilateral stenosis of renal arteries resulting in renovascular hypertension. His hypertension was difficult to control medically and autotransplant of his kidneys to the iliac arteries was performed, but he died in the immediate postoperative period. The relationship between immunodeficiency and collagen-vascular disease was discussed. |
| Databáze: | OpenAIRE |
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