The Windsock Syndrome: Subpulmonic Obstruction by Membranous Ventricular Septal Aneurysm in Congenitally Corrected Transposition of Great Arteries

Autor: Robert M. Applebaum, Charles Okamura, Louai Razzouk, Muhamed Saric
Rok vydání: 2013
Předmět:
Zdroj: Echocardiography. 30:E243-E248
ISSN: 0742-2822
DOI: 10.1111/echo.12279
Popis: Anomalies of the membranous portion of the interventricular septum include perimembranous ventricular septal defect and/or membranous septal aneurysm (MSA). In congenitally corrected transposition of the great arteries (L-TGA in sinus solitus), the combination of ventricular inversion and arterial transposition creates a unique anatomic substrate that fosters subpulmonic left ventricular outflow tract obstruction by an MSA. The combination of an L-TGA with subpulmonic obstruction by an MSA is referred to as the windsock syndrome. We report a case of windsock syndrome in a 25-year-old man which is to our knowledge the first three-dimensional echocardiographic description of this congenital entity.
Databáze: OpenAIRE
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