Parry-Romberg syndrome in a patient with scleroderma
| Autor: | Chii Yang Kuah, Jaslyn Ju Lia Gan, Elena Koleva, Tahir Iqbal |
|---|---|
| Rok vydání: | 2018 |
| Předmět: |
Reconstructive surgery
medicine.medical_specialty Scleroderma 030207 dermatology & venereal diseases 03 medical and health sciences Scleroderma Localized 0302 clinical medicine Rare Disease Internal medicine Facial Hemiatrophy medicine Humans Neck stiffness business.industry Parry–Romberg syndrome General Medicine Middle Aged medicine.disease Dermatology Hyperpigmentation Rheumatology stomatognathic diseases Methotrexate Female Dermatologic Agents Headaches medicine.symptom business 030217 neurology & neurosurgery Rare disease |
| Zdroj: | BMJ Case Rep |
| ISSN: | 1757-790X |
| Popis: | Parry-Romberg syndrome (PRS) is characterised by progressive but self-limiting facial hemiatrophy. We describe a 48-year-old woman with a 3-year history of gradually worsening right facial hemiatrophy on a background of scleroderma. Her initial primary concern was alopecia. Within the last year, there was greater prominence of her right zygoma and hyperpigmentation on her forearms and left neck. She also had worsening headaches and neck stiffness in the mornings. A clinical diagnosis of PRS was made and she was subsequently treated with a course of methotrexate. She is due to be followed up by dermatology, rheumatology and maxillofacial surgery with the aim of reconstructive surgery once her symptoms stabilise. |
| Databáze: | OpenAIRE |
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