Surgical significance of the Ehlers-Danlos syndrome

Autor: F.James Rybka, Edward T. O'Hara
Rok vydání: 1967
Předmět:
Zdroj: The American Journal of Surgery. 113:431-434
ISSN: 0002-9610
DOI: 10.1016/0002-9610(67)90295-4
Popis: Bleeding from major arteries is the most formidable complication encountered in Ehlers-Danlos syndrome and results from fragility of the vessels as well as the lack of tamponade by the adjacent connective tissue structures. A case is presented to illustrate this, and the literature is reviewed to show that hemorrhage might result from surgery or from trauma which sometimes is very trivial. Young men seem to be predominantly affected. Other complications include wound dehiscence and perforation of the bowel. It is important that those afflicted be aware of the dangers of trauma and that their physicians be aware of their unusual tissues.
Databáze: OpenAIRE