Surgical Correction of Supravalvar Aortic Stenosis
| Autor: | Joost P. van Melle, Mark G. Hazekamp, Jolanda Kluin, Sara C. Arrigoni, Rosa Roemers, Frederiek de Heer, Regina Bökenkamp, Tjark Ebels |
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| Přispěvatelé: | Cardiovascular Centre (CVC), ACS - Atherosclerosis & ischemic syndromes, Cardiothoracic Surgery, Graduate School, ACS - Heart failure & arrhythmias |
| Jazyk: | angličtina |
| Rok vydání: | 2018 |
| Předmět: |
Adult
Male Reoperation medicine.medical_specialty supravalvar aortic stenosis Adolescent Williams syndrome ELASTIN GENE CHILDREN 030204 cardiovascular system & hematology 3-PATCH TECHNIQUE Young Adult 03 medical and health sciences 0302 clinical medicine medicine Humans supravalvular aortic stenosis Child Aorta Sinus (anatomy) Retrospective Studies REPAIR OUTCOMES business.industry Infant Newborn Infant General Medicine Original Articles Middle Aged Surgical correction medicine.disease Aortic Stenosis Supravalvular Stenosis Treatment Outcome medicine.anatomical_structure 030228 respiratory system three-patch technique AORTOPLASTY Child Preschool Pediatrics Perinatology and Child Health Female Surgery Radiology Cardiology and Cardiovascular Medicine business Vascular Surgical Procedures Supravalvular aortic stenosis Follow-Up Studies |
| Zdroj: | World Journal for Pediatric & Congenital Heart Surgery World journal for pediatric and congenital heart surgery, 9(2), 131-138. SAGE Publications Inc. World Journal for Pediatric and Congenital Heart Surgery, 9(2), 131-138 World journal for pediatric & congenital heart surgery, 9(2), 131-138. Sage Periodicals Press |
| ISSN: | 2150-1351 2150-136X |
| Popis: | Objectives: Supravalvar aortic stenosis (SVAS) is a rare congenital anomaly. The “single-patch technique,” “‘two sinus augmentation with an inverted Y-patch” (both nonsymmetrical corrections), “three-patch technique,” and the “slide aortoplasty” (both symmetrical corrections) are the techniques implemented by the majority of surgeons for the correction of SVAS. In the few studies that compared these techniques, no technique was shown to be superior over another. The aim of the present study is to review the 52-year experience with the surgical correction of SVAS in two of four congenital cardiothoracic surgical centers in the Netherlands. Methods: We retrospectively reviewed all patient files of those who underwent an operation to correct their SVAS, between 1962 and 2014 in our centers. Patients were divided according to their operating technique. These groups were compared using the end points freedom from reoperation and mortality. Results: A total of 49 patients were included, 23 (46.9%) patients in the nonsymmetrical group and 26 (53.1%) patients in the symmetrical group. Survival after 20 years in the nonsymmetrical group was 80% (standard error [SE]: 0.091) and in the symmetrical group was 85% (SE: 0.085; P = .163). Freedom from reoperation after 20 years in the nonsymmetrical group was 88% (SE: 0.079) and in the symmetrical group was 71% (SE: 0.107; P = 0.313). Conclusion: In this patient group, there is no significant difference in survival and freedom from reoperation between the different surgical techniques for SVAS repair. Compared to the survival in the general population, the survival of SVAS patients is remarkably low. Apparently, SVAS is not a benign disease and probably patients should be followed more closely for the rest of their lives. |
| Databáze: | OpenAIRE |
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