Evans Syndrome in a Jehovah’s Witness
Autor: | Alejandro Calvo, Lex P Leonhardt, Aamir Pervez |
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Rok vydání: | 2021 |
Předmět: |
Pediatrics
medicine.medical_specialty Evans syndrome Jehovah s witness idiopathic thrombocytopenia thrombocytopenia Neutropenia Dyscrasia Allergy/Immunology Blood product hemic and lymphatic diseases Internal Medicine medicine microangiopathic autoimmune hemolytic anemia evans syndrome biology business.industry transfusion refusal General Engineering Hematology medicine.disease jehovah's witness biology.protein Autoimmune hemolytic anemia Antibody blood dyscrasia business Idiopathic thrombocytopenia |
Zdroj: | Cureus |
ISSN: | 2168-8184 |
DOI: | 10.7759/cureus.15508 |
Popis: | Evans syndrome (ES) is a rare hematologic disorder characterized by the development of autoimmune hemolytic anemia (AIHA), idiopathic thrombocytopenia, and occasionally immune-mediated neutropenia. Jehovah’s Witnesses (JW) often decline blood product transfusion on the grounds of a scriptural stand based on biblical texts. The acute management of ES often consists of blood product transfusion in addition to high-dose steroids and intravenous immunoglobulin. We describe the case of a JW female presenting with new-onset, acutely worsening AIHA and thrombocytopenia with concern for hemodynamic compromise who was successfully treated with erythropoietin-stimulating agents, parenteral iron, folic acid, and high-dose steroids. |
Databáze: | OpenAIRE |
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