Scleredema with biopsy-confirmed cardiomyopathy: A case report
| Autor: | Naoto Ishimaru, Saori Kinami, Nobuya Sano, Kei Kawano, Mei Nakatsuji, Shimpei Mizuki, Takahiro Nakajima, Jun Ohnishi, Masaru Kuroda, Yohei Kanzawa |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2021 |
| Předmět: |
030203 arthritis & rheumatology
Pathology medicine.medical_specialty Myocardial biopsy medicine.diagnostic_test Skin thickening business.industry Immunology Cardiomyopathy Case Reports medicine.disease Trunk Mucinosis 03 medical and health sciences 0302 clinical medicine Rheumatology Biopsy medicine Scleredema Immunology and Allergy 030212 general & internal medicine business |
| Zdroj: | J Scleroderma Relat Disord |
| Popis: | Scleredema is a rare cutaneous mucinosis characterized by diffuse swelling and non-pitting induration. A 63-year-old man reported a 5-year history of skin thickening of the trunk and a 3-week history of dyspnea. Echocardiography revealed diffuse hypokinesis. Skin biopsies obtained from the waist showed thickened dermis with mucin. Myocardial biopsies showed alcian blue-stained tissue between the muscle fibers. The patient was referred to a dermatologist for phototherapy. Cardiomyopathy should be considered in patients with scleredema. Scleredema usually has a good prognosis; however, the mortality risk could be high when accompanied by cardiomyopathy. |
| Databáze: | OpenAIRE |
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